EC Number   |
Natural Substrates |
|---|
    2.3.1.1 | acetyl-CoA + L-glutamate |
- |
| 2.3.1.1 | acetyl-CoA + L-glutamate |
ability of protein Cg3035 to acetylate L-glutamate in vitro and in vivo |
| 2.3.1.1 | more |
autosomal recessively inherited enzyme deficiency causes severe neonatal or late-onset hyperammonemia, the enzyme is an allosteric activator of the carbamoylphosphate synthase I, the first enzyme of the urea cycle |
| 2.3.1.1 | acetyl-CoA + L-glutamate |
enzyme activates carbamoyl-phosphate synthase ammonia in small intestine mucosa, to allow citrulline synthesis in the tissue |
| 2.3.1.1 | acetyl-CoA + L-glutamate |
enzyme catalyzes the first step in arginine biosynthesis |
| 2.3.1.1 | acetyl-CoA + L-glutamate |
enzyme catalyzes the first step in the biosynthesis of arginine |
| 2.3.1.1 | more |
enzyme deficiency causes hyperammonemia, presumably due to loss of carbamoylphosphate synthase I activity |
| 2.3.1.1 | acetyl-CoA + L-glutamate |
first enzyme in urea cycle |
| 2.3.1.1 | acetyl-CoA + L-glutamate |
indispensible enzyme of arginine biosynthesis |
| 2.3.1.1 | acetyl-CoA + L-glutamate |
initial step of the L-arginine biosynthesis, pathway overview |
