EC Number   |
Specific Activity Minimum [µmol/min/mg] |
Specific Activity Maximum [µmol/min/mg] |
Reference |
|---|
    1.3.8.4 | -999 |
- |
enzyme assay development and optimization |
655248 |
| 1.3.8.4 | 0.00003 |
- |
intact mitochondria, no added acceptor |
391204 |
| 1.3.8.4 | 0.000039 |
- |
mitochondria from isovaleric acidemia cells, 13% relative activity to normal cells, specific activity determined by tritium release assay |
391206 |
| 1.3.8.4 | 0.00016 |
- |
sonicated mitochondria, no added acceptor |
391204 |
| 1.3.8.4 | 0.000163 |
- |
mitochondria from isovaleric acidemia cells, 12% relative activity to normal cells, specific activity determined by dye reduction assay |
391206 |
| 1.3.8.4 | 0.0003 |
- |
recombinant mutant L95V/A99V/L103V/L370M/G374A, substrate 2-methylbutanoyl-CoA |
656288 |
| 1.3.8.4 | 0.00031 |
- |
mitochondria from normal cells, specific activity determined by tritium release assay |
391206 |
| 1.3.8.4 | 0.00034 |
- |
fibroblast cell line harboring the mutation corresponding to the A282V mutant |
391212 |
| 1.3.8.4 | 0.00044 |
- |
sonicated mitochondria, acceptor added: electron-transferring flavoprotein |
391204 |
| 1.3.8.4 | 0.00046 |
- |
sonicated mitochondria, acceptor added: phenazine methosulfate |
391204 |
