EC Number |
Recommended Name |
Localization |
GeneOntology No. |
Reference |
---|
1.1.1.1 | alcohol dehydrogenase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
684960 |
1.1.1.35 | 3-hydroxyacyl-CoA dehydrogenase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
739806, 741307 |
1.11.1.9 | glutathione peroxidase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
396604, 396617 |
1.11.1.9 | glutathione peroxidase |
mitochondrial matrix |
25% of activity |
GO:0005759 AmiGO QuickGO |
396627 |
1.13.11.18 | persulfide dioxygenase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
713090 |
1.15.1.1 | superoxide dismutase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
715260 |
1.15.1.1 | superoxide dismutase |
mitochondrial matrix |
isoenzyme Mn-SOD, specifically |
GO:0005759 AmiGO QuickGO |
-, 684757 |
1.15.1.1 | superoxide dismutase |
mitochondrial matrix |
MnSOD is translated in the cytoplasm and then imported into the mitochondria via a mitochondrial targeting signal |
GO:0005759 AmiGO QuickGO |
716197 |
1.2.1.105 | 2-oxoglutarate dehydrogenase system |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
724891 |
1.2.1.24 | succinate-semialdehyde dehydrogenase (NAD+) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
710898, 743762 |
1.2.1.27 | methylmalonate-semialdehyde dehydrogenase (CoA-acylating) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
-, 675669 |
1.4.1.3 | glutamate dehydrogenase [NAD(P)+] |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
686680 |
1.5.1.10 | saccharopine dehydrogenase (NADP+, L-glutamate-forming) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
763097 |
1.5.1.10 | saccharopine dehydrogenase (NADP+, L-glutamate-forming) |
mitochondrial matrix |
in Arabidopsis, a monofunctional SDH probably produced from the same gene encoding the bifunctional enzyme localizes in the mitochondria |
GO:0005759 AmiGO QuickGO |
763097 |
1.5.1.2 | pyrroline-5-carboxylate reductase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
654887 |
1.5.1.8 | saccharopine dehydrogenase (NADP+, L-lysine-forming) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
763097 |
1.5.1.8 | saccharopine dehydrogenase (NADP+, L-lysine-forming) |
mitochondrial matrix |
enzyme found only in the mitochondrial matrix |
GO:0005759 AmiGO QuickGO |
392366 |
1.5.1.9 | saccharopine dehydrogenase (NAD+, L-glutamate-forming) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
763097 |
1.5.1.9 | saccharopine dehydrogenase (NAD+, L-glutamate-forming) |
mitochondrial matrix |
in Arabidopsis, a monofunctional SDH probably produced from the same gene encoding the bifunctional enzyme localizes in the mitochondria |
GO:0005759 AmiGO QuickGO |
763097 |
1.5.3.16 | spermine oxidase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
742563 |
1.5.3.17 | non-specific polyamine oxidase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
742563 |
1.5.8.4 | dimethylglycine dehydrogenase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
742499 |
2.1.1.201 | 2-methoxy-6-polyprenyl-1,4-benzoquinol methylase |
mitochondrial matrix |
peripherally associated with the inner mitochondrial membrane on the matrix side |
GO:0005759 AmiGO QuickGO |
704408 |
2.1.1.228 | tRNA (guanine37-N1)-methyltransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
687609 |
2.1.2.10 | aminomethyltransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
391984 |
2.1.3.3 | ornithine carbamoyltransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
-, 719326, 736014 |
2.3.1.35 | glutamate N-acetyltransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
486801, 486803, 486806 |
2.3.1.37 | 5-aminolevulinate synthase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
486818, 486823 |
2.3.1.7 | carnitine O-acetyltransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
487402, 487418, 487426, 487432, 659194, 659815, 736560 |
2.3.1.B43 | protein-lysine desuccinylase (NAD+) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
703149, 728932, 757590 |
2.3.1.B43 | protein-lysine desuccinylase (NAD+) |
mitochondrial matrix |
predominantly |
GO:0005759 AmiGO QuickGO |
756522 |
2.3.3.5 | 2-methylcitrate synthase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
488089 |
2.5.1.18 | glutathione transferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
721532 |
2.6.1.13 | ornithine aminotransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
637137 |
2.6.1.7 | kynurenine-oxoglutarate transaminase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
439375 |
2.7.1.113 | deoxyguanosine kinase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
640559, 661453, 663023 |
2.7.1.86 | NADH kinase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
-, 759283 |
2.7.11.2 | [pyruvate dehydrogenase (acetyl-transferring)] kinase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
642137, 721523, 722148 |
2.7.11.2 | [pyruvate dehydrogenase (acetyl-transferring)] kinase |
mitochondrial matrix |
BCR-ABL, JAK2, and FLT3 are co-localized with PDHK1 |
GO:0005759 AmiGO QuickGO |
723186 |
2.7.11.4 | [3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
640581, 762211 |
2.7.11.4 | [3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase |
mitochondrial matrix |
2 forms: first form is bound to E2, second form is free and seems to be inactive |
GO:0005759 AmiGO QuickGO |
640597 |
2.7.4.10 | nucleoside-triphosphate-adenylate kinase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
662361 |
2.7.4.9 | dTMP kinase |
mitochondrial matrix |
low levels of canonical TMPK protein |
GO:0005759 AmiGO QuickGO |
759870 |
2.7.7.1 | nicotinamide-nucleotide adenylyltransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
705288 |
2.7.7.7 | DNA-directed DNA polymerase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
723132 |
2.8.1.1 | thiosulfate sulfurtransferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
725406 |
2.8.1.7 | cysteine desulfurase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
-, 645615, 645622, 661595 |
2.8.3.5 | 3-oxoacid CoA-transferase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
762068 |
3.1.1.1 | carboxylesterase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
-, 750612 |
3.1.2.18 | ADP-dependent short-chain-acyl-CoA hydrolase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
646112 |
3.1.2.18 | ADP-dependent short-chain-acyl-CoA hydrolase |
mitochondrial matrix |
submitochondrial distribution |
GO:0005759 AmiGO QuickGO |
646111 |
3.1.2.19 | ADP-dependent medium-chain-acyl-CoA hydrolase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
646111, 646112 |
3.1.2.6 | hydroxyacylglutathione hydrolase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
716929 |
3.1.2.6 | hydroxyacylglutathione hydrolase |
mitochondrial matrix |
mitochondrial isozyme is targeted directly to the mitochondrial matrix due to a mitochondrial targeting sequence |
GO:0005759 AmiGO QuickGO |
652549 |
3.1.4.17 | 3',5'-cyclic-nucleotide phosphodiesterase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
750418 |
3.2.1.26 | beta-fructofuranosidase |
mitochondrial matrix |
highest invertase activities compared to inner or outer membrane, since transport capacity through matrix is limiting enzyme activity, enzyme must be located on inner matrix |
GO:0005759 AmiGO QuickGO |
700860 |
3.4.21.53 | Endopeptidase La |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
732470 |
3.4.21.89 | Signal peptidase I |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
29815 |
3.4.24.59 | mitochondrial intermediate peptidase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
31356, 31357 |
3.4.24.64 | mitochondrial processing peptidase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
733399, 733944 |
3.4.24.64 | mitochondrial processing peptidase |
mitochondrial matrix |
beta and alpha subunit of MPP, Western blot of the mitochondrial subfractions |
GO:0005759 AmiGO QuickGO |
696812 |
3.5.3.6 | arginine deiminase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
209455 |
3.6.1.13 | ADP-ribose diphosphatase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
209862 |
3.6.4.10 | non-chaperonin molecular chaperone ATPase |
mitochondrial matrix |
Hsp70 |
GO:0005759 AmiGO QuickGO |
210500 |
3.6.4.10 | non-chaperonin molecular chaperone ATPase |
mitochondrial matrix |
mainly |
GO:0005759 AmiGO QuickGO |
734351 |
4.1.1.9 | malonyl-CoA decarboxylase |
mitochondrial matrix |
INS-1 MCD, expression most likely in, contains an N-terminal mitochondrial targeting sequence |
GO:0005759 AmiGO QuickGO |
649668 |
4.1.3.30 | Methylisocitrate lyase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
651674 |
4.4.1.9 | L-3-cyanoalanine synthase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
730655 |
5.3.2.2 | oxaloacetate tautomerase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
2875, 2877, 2878, 2880 |
5.3.2.2 | oxaloacetate tautomerase |
mitochondrial matrix |
about 30% of the tautomerase activity in the matrix are represented by oxaloacetate tautomerase-1 and about 70% by oxaloacetate tautomerase-2 |
GO:0005759 AmiGO QuickGO |
2879 |
5.4.99.2 | methylmalonyl-CoA mutase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
3508, 3518 |
5.6.2.3 | DNA 5'-3' helicase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
757877 |
6.2.1.4 | succinate-CoA ligase (GDP-forming) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
693488, 782 |
6.2.1.5 | succinate-CoA ligase (ADP-forming) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
693488 |
6.3.2.12 | dihydrofolate synthase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
653665 |
6.3.4.16 | carbamoyl-phosphate synthase (ammonia) |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
1455, 693247 |
6.3.4.16 | carbamoyl-phosphate synthase (ammonia) |
mitochondrial matrix |
15-20% of the total mitochondrial protein |
GO:0005759 AmiGO QuickGO |
1468 |
6.3.4.16 | carbamoyl-phosphate synthase (ammonia) |
mitochondrial matrix |
constitutes 22-26% of the total matrix protein |
GO:0005759 AmiGO QuickGO |
1456 |
6.3.4.16 | carbamoyl-phosphate synthase (ammonia) |
mitochondrial matrix |
the N-terminal targeting signal normally directs the nuclear-encoded protein to the mitochondrial matrix and is cleaved as the protein enters the matrix |
GO:0005759 AmiGO QuickGO |
693489 |
6.4.1.1 | pyruvate carboxylase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
690828, 694200 |
6.4.1.4 | methylcrotonoyl-CoA carboxylase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
660914 |
6.4.1.4 | methylcrotonoyl-CoA carboxylase |
mitochondrial matrix |
soluble matrix |
GO:0005759 AmiGO QuickGO |
1895 |
7.4.2.3 | mitochondrial protein-transporting ATPase |
mitochondrial matrix |
- |
GO:0005759 AmiGO QuickGO |
686245, 687560, 689911 |