5.4.99.2 Acidosis http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=15647267&form=6&db=m Nitric oxide inhibits mammalian methylmalonyl-CoA mutase. causal interaction,unassigned 4,0 5.4.99.2 Acidosis http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=26077484&form=6&db=m Early Liver Transplantation for Neonatal-Onset Methylmalonic Acidemia. causal interaction,unassigned 3,0 5.4.99.2 acyl-coa dehydrogenase deficiency http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=2507694&form=6&db=m Vitamins and inherited human errors of metabolism. causal interaction,unassigned 2,0 5.4.99.2 Argininosuccinic Aciduria http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=26589311&form=6&db=m Inborn Errors of Metabolism in the United Arab Emirates: Disorders Detected by Newborn Screening (2011-2014). causal interaction,diagnostic usage,unassigned 2,3,0 5.4.99.2 Ataxia http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=8789622&form=6&db=m Effect of N2O treatment/vitamin B12 deficiency in pigs on tissue concentrations of odd-numbered, branched-chain fatty acids. diagnostic usage,ongoing research,unassigned 1,2,0 5.4.99.2 biotin-[propionyl-coa-carboxylase (atp-hydrolysing)] ligase deficiency http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=2507694&form=6&db=m Vitamins and inherited human errors of metabolism. causal interaction,unassigned 2,0 5.4.99.2 biotinidase deficiency http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=26589311&form=6&db=m Inborn Errors of Metabolism in the United Arab Emirates: Disorders Detected by Newborn Screening (2011-2014). causal interaction,causal interaction,diagnostic usage,diagnostic usage,unassigned,unassigned 2,2,3,3,0,0 5.4.99.2 Brain Ischemia http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=8929440&form=6&db=m Methylmalonyl-CoA mutase induction by cerebral ischemia and neurotoxicity of the mitochondrial toxin methylmalonic acid. unassigned - 5.4.99.2 branched-chain-2-oxoacid decarboxylase deficiency http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=1016232&form=6&db=m Demonstration of a new mammalian isoleucine catabolic pathway yielding an Rseries of metabolites. causal interaction,unassigned 4,0 5.4.99.2 Coma http://www.ncbi.nlm.nih.gov/htbin-post/Entrez/query?uid=26077484&form=6&db=m Early Liver Transplantation for Neonatal-Onset Methylmalonic Acidemia. causal interaction,unassigned 3,0