4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/1355046/	7-substituted pterins in humans with suspected pterin-4a-carbinolamine dehydratase deficiency. Mechanism of formation via non-enzymatic transformation from 6-substituted pterins.	causal interaction	2	
4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/1405480/	Suspected pterin-4a-carbinolamine dehydratase deficiency: hyperphenylalaninaemia due to inhibition of phenylalanine hydroxylase by tetrahydro-7-biopterin.	causal interaction	3	
4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/8830181/	International database of tetrahydrobiopterin deficiencies.	causal interaction	3	
4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/11937441/	[Screening of tetrahydrobiopterin deficiency among hyperphenylalaninemic patients]	diagnostic usage	3	
4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/11937441/	[Screening of tetrahydrobiopterin deficiency among hyperphenylalaninemic patients]	unassigned	-	
4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/1355046/	7-substituted pterins in humans with suspected pterin-4a-carbinolamine dehydratase deficiency. Mechanism of formation via non-enzymatic transformation from 6-substituted pterins.	unassigned	-	
4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/1405480/	Suspected pterin-4a-carbinolamine dehydratase deficiency: hyperphenylalaninaemia due to inhibition of phenylalanine hydroxylase by tetrahydro-7-biopterin.	unassigned	-	
4.2.1.96	4a-hydroxytetrahydrobiopterin dehydratase deficiency	https://pubmed.ncbi.nlm.nih.gov/8830181/	International database of tetrahydrobiopterin deficiencies.	unassigned	-	
4.2.1.96	6,7-dihydropteridine reductase deficiency	https://pubmed.ncbi.nlm.nih.gov/8830181/	International database of tetrahydrobiopterin deficiencies.	causal interaction	3	
4.2.1.96	6,7-dihydropteridine reductase deficiency	https://pubmed.ncbi.nlm.nih.gov/8830181/	International database of tetrahydrobiopterin deficiencies.	unassigned	-