EC Number | Cloned (Comment) | Organism |
---|---|---|
4.1.1.112 | expressed in Mus musculus | Homo sapiens |
EC Number | Protein Variants | Comment | Organism |
---|---|---|---|
4.1.1.112 | D102A/R106A | the mutant shows about 3% of wild type activity | Homo sapiens |
4.1.1.112 | E33A | the mutant shows about 40% of wild type activity | Homo sapiens |
4.1.1.112 | H30A | the mutant shows about 20% of wild type activity | Homo sapiens |
EC Number | Inhibitors | Comment | Organism | Structure |
---|---|---|---|---|
4.1.1.112 | oxalate | potent competitive inhibition | Homo sapiens |
EC Number | KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|---|
4.1.1.112 | 0.032 | - |
oxaloacetate | at pH 7.4 and 25°C | Homo sapiens |
EC Number | Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
4.1.1.112 | fumarylpyruvate + H2O | Homo sapiens | - |
fumarate + pyruvate + H+ | - |
? | |
4.1.1.112 | oxaloacetate + H+ | Homo sapiens | - |
pyruvate + CO2 | - |
? |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
4.1.1.112 | Homo sapiens | Q6P587 | - |
- |
EC Number | Purification (Comment) | Organism |
---|---|---|
4.1.1.112 | - |
Homo sapiens |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
4.1.1.112 | fumarylpyruvate + H2O | - |
Homo sapiens | fumarate + pyruvate + H+ | - |
? | |
4.1.1.112 | oxaloacetate + H+ | - |
Homo sapiens | pyruvate + CO2 | - |
? |
EC Number | Subunits | Comment | Organism |
---|---|---|---|
4.1.1.112 | homodimer | 2 * 29000, SDS-PAGE | Homo sapiens |
EC Number | Synonyms | Comment | Organism |
---|---|---|---|
4.1.1.112 | FAH domain-containing protein 1 | - |
Homo sapiens |
4.1.1.112 | FAHD1 | - |
Homo sapiens |
4.1.1.112 | fumarylacetoacetate hydrolase domain-containing protein 1 | - |
Homo sapiens |
4.1.1.112 | ODx | - |
Homo sapiens |
EC Number | Ki Value [mM] | Ki Value maximum [mM] | Inhibitor | Comment | Organism | Structure |
---|---|---|---|---|---|---|
4.1.1.112 | 0.001 | - |
oxalate | at pH 7.4 and 25°C | Homo sapiens |