EC Number | Metals/Ions | Comment | Organism | Structure |
---|---|---|---|---|
2.4.1.228 | Mn2+ | - |
Homo sapiens |
EC Number | Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
2.4.1.228 | UDP-galactose + beta-D-galactosyl-(1-4)-D-glucosylceramide | Homo sapiens | - |
UDP + alpha-D-galactosyl-(1-4)-beta-D-galactosyl-(1-4)-D-glucosylceramide | - |
? |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
2.4.1.228 | Homo sapiens | - |
- |
- |
EC Number | Source Tissue | Comment | Organism | Textmining |
---|---|---|---|---|
2.4.1.228 | Fanconi anemia lymphoid cell line | blood of a small p subject and a P1 control subject | Homo sapiens | - |
EC Number | Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|---|
2.4.1.228 | additional information | - |
- |
Homo sapiens |
EC Number | Storage Stability | Organism |
---|---|---|
2.4.1.228 | -20°C | Homo sapiens |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
2.4.1.228 | UDP-galactose + beta-D-galactosyl-(1-4)-D-glucosylceramide | - |
Homo sapiens | UDP + alpha-D-galactosyl-(1-4)-beta-D-galactosyl-(1-4)-D-glucosylceramide | - |
? | |
2.4.1.228 | UDP-galactose + lactosylceramide | in the small p cells in vitro only | Homo sapiens | UDP + globotriaosylceramide | - |
? |
EC Number | Temperature Optimum [°C] | Temperature Optimum Maximum [°C] | Comment | Organism |
---|---|---|---|---|
2.4.1.228 | 37 | - |
enzyme assay | Homo sapiens |