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Literature summary extracted from

  • Kelson, T.L.; Ohura, T.; Kraus, J.P.
    Chaperonin-mediated assembly of wild-type and mutant subunits of human propionyl-CoA carboxylase expressed in Escherichia coli (1996), Hum. Mol. Genet., 5, 331-337.
    View publication on PubMed

Cloned(Commentary)

EC Number Cloned (Comment) Organism
6.4.1.3 expression of alpha and beta subunit in Escherichia coli Homo sapiens

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
6.4.1.3 additional information Homo sapiens inherited deficiency of the enzyme activity leads to propionicacidemia ?
-
?

Organism

EC Number Organism UniProt Comment Textmining
6.4.1.3 Homo sapiens
-
-
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
6.4.1.3 ATP + propanoyl-CoA + HCO3-
-
Homo sapiens ADP + phosphate + methylmalonyl-CoA
-
?
6.4.1.3 additional information inherited deficiency of the enzyme activity leads to propionicacidemia Homo sapiens ?
-
?