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Literature summary for 7.2.2.9 extracted from

  • Lutsenko, S.; Efremov, R.G.; Tsivkovskii, R.; Walker, J.M.
    Human copper-transporting ATPase ATP7B (the Wilson's disease protein): biochemical properties and regulation (2002), J. Bioenerg. Biomembr., 34, 351-362.
    View publication on PubMed

Cloned(Commentary)

Cloned (Comment) Organism
expression in Saccharomyces cerevisiae Homo sapiens

Localization

Localization Comment Organism GeneOntology No. Textmining
Golgi trans face
-
Homo sapiens
-
-

Metals/Ions

Metals/Ions Comment Organism Structure
Cu2+ six binding sites, regulates enzyme modulating catalytic activity, posttranslational modification and intracellular localization Homo sapiens

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Posttranslational Modification

Posttranslational Modification Comment Organism
phosphoprotein two phosphorilation sites, phosphorilation is induced by copper Homo sapiens

Source Tissue

Source Tissue Comment Organism Textmining

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
ATP + H2O + Cu2+/in
-
Homo sapiens ADP + phosphate + Cu2+/out
-
r

Synonyms

Synonyms Comment Organism
ATP7B
-
Homo sapiens
Wilson's disease protein
-
Homo sapiens
WNDP
-
Homo sapiens