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Literature summary for 7.1.1.9 extracted from

  • Kovarova, N.; Pecina, P.; Nuskova, H.; Vrbacky, M.; Zeviani, M.; Mracek, T.; Viscomi, C.; Houstek, J.
    Tissue- and species-specific differences in cytochrome c oxidase assembly induced by SURF1 defects (2016), Biochim. Biophys. Acta, 1862, 705-715 .
    View publication on PubMedView publication on EuropePMC

Localization

Localization Comment Organism GeneOntology No. Textmining
mitochondrion
-
Mus musculus 5739
-
mitochondrion
-
Homo sapiens 5739
-

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
ferrocytochrome c + O2 + H+ Mus musculus
-
ferricytochrome c + H2O
-
?
ferrocytochrome c + O2 + H+ Homo sapiens
-
ferricytochrome c + H2O
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
brain
-
Mus musculus
-
fibroblast
-
Mus musculus
-
fibroblast
-
Homo sapiens
-
heart
-
Mus musculus
-
liver
-
Mus musculus
-
muscle
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
ferrocytochrome c + O2 + H+
-
Mus musculus ferricytochrome c + H2O
-
?
ferrocytochrome c + O2 + H+
-
Homo sapiens ferricytochrome c + H2O
-
?

Synonyms

Synonyms Comment Organism
COX
-
Mus musculus
COX
-
Homo sapiens
cytochrome c oxidase
-
Mus musculus
cytochrome c oxidase
-
Homo sapiens

General Information

General Information Comment Organism
malfunction enzyme deficiency manifests as the Leigh syndrome in humans Homo sapiens