Cloned (Comment) | Organism |
---|---|
expression in Escherichia coli | Homo sapiens |
Crystallization (Comment) | Organism |
---|---|
hanging-drop vapor diffusion, crystal structure of Q286R mutant at 2.65 A | Homo sapiens |
Protein Variants | Comment | Organism |
---|---|---|
Q286R | frequently complementing allele, 2% of wild-type kcat | Homo sapiens |
R12Q | 6% of wild-type kcat | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.12 | - |
N,N'-bis(tert-butoxycarbonyl)-5-[(3-aminopropyl)amino]pentan-1-ol | pH 7.6 | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
(Nomega-L-arginino)succinate | Homo sapiens | - |
fumarate + L-arginine | - |
r |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
mutations in ASL result in the clinical condition argininosuccinic aciduria, an autosomal recessive disorder | - |
Purification (Comment) | Organism |
---|---|
recombinant ASL | Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
(Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
? | |
(Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
r | |
N,N'-bis(tert-butoxycarbonyl)-5-[(3-aminopropyl)amino]pentan-1-ol | - |
Homo sapiens | ? | - |
? |
Synonyms | Comment | Organism |
---|---|---|
ASL | - |
Homo sapiens |
Turnover Number Minimum [1/s] | Turnover Number Maximum [1/s] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
34.5 | - |
N,N'-bis(tert-butoxycarbonyl)-5-[(3-aminopropyl)amino]pentan-1-ol | pH 7.6 | Homo sapiens |