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Literature summary for 3.4.22.54 extracted from

  • Kramerova, I.; Kudryashova, E.; Wu, B.; Germain, S.; Vandenborne, K.; Romain, N.; Haller, R.G.; Verity, M.A.; Spencer, M.J.
    Mitochondrial abnormalities, energy deficit and oxidative stress are features of calpain 3 deficiency in skeletal muscle (2009), Hum. Mol. Genet., 18, 3194-3205.
    View publication on PubMedView publication on EuropePMC
Search for more literature for 3.4.22.54

Protein Variants

Protein Variants Comment Organism
C129S inactive Mus musculus

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
55000
-
 full-length CAPN3 undergoes almost complete autolysis and runs as a 55 kDa band, SDS-PAGE Mus musculus

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
skeletal muscle
-
 Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
additional information calpain-3 does not cleave acetyl-coenzyme A acyltransferase, carnitine O-palmitoyl transferase II, carnitine acetyltransferase, and trifunctional protein alpha subunit Mus musculus ?
-
 ?
very long chain acyl-coenzyme A dehydrogenase + H2O an in vivo substrate for calpain-3 Mus musculus ?
-
 ?

Synonyms

Synonyms Comment Organism
calpain 3
-
 Mus musculus
CAPN3
-
 Mus musculus

General Information

General Information Comment Organism
malfunction mitochondrial abnormalities, energy deficit and oxidative stress are features of calpain 3 deficiency in skeletal muscle Mus musculus