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Literature summary for 3.1.2.22 extracted from

  • Cho, S.; Dawson, G.
    Enzymatic and molecular biological analysis of palmitoyl protein thioesterase deficiency in infantile neuronal ceroid lipofuscinosis (1998), J. Neurochem., 71, 323-329.
    View publication on PubMed

Application

Application Comment Organism
medicine in vitro enzyme assay that can be readily used for the clinical diagnosis of both infantile neuronal ceroid lipofuscinosis patients and carrier Homo sapiens

Localization

Localization Comment Organism GeneOntology No. Textmining
lysosome
-
Homo sapiens 5764
-

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
HEK-293 cell
-
Homo sapiens
-
Hep-G2 cell
-
Homo sapiens
-
LAN5 cell
-
Homo sapiens
-
oligodendroglioma cell
-
Homo sapiens
-
skin fibroblast
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
palmitoyl-[protein] + H2O
-
Homo sapiens palmitate + protein
-
?

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
5
-
-
Homo sapiens