Cloned (Comment) | Organism |
---|---|
- |
Homo sapiens |
General Stability | Organism |
---|---|
enzyme is only soluble under denaturating conditions | Homo sapiens |
Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|
52000 | - |
SDS-PAGE | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
succinyl-CoA + acetoacetate | Homo sapiens | enzyme deficiency leads to ketoacidotic crises and persistent ketosis | ? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
SCOT-deficient patients | - |
Homo sapiens | - |
healthy and SCOT-deficient patients | - |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
fibroblast | - |
Homo sapiens | - |
lymphocyte | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
succinyl-CoA + acetoacetate | - |
Homo sapiens | succinate + acetoacetyl-CoA | - |
? | |
succinyl-CoA + acetoacetate | enzyme deficiency leads to ketoacidotic crises and persistent ketosis | Homo sapiens | ? | - |
? |