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Literature summary for 2.8.3.5 extracted from

  • Song, X.Q.; Fukao, T.; Mitchell, G.A.; Kassovska-Bratinova, S.; Ugarte, M.; Wanders, R.J.; Hirayama, K.; Shintaku, H.; Churchill, P.; Watanabe, H.; Orii, T.; Kondo, N.
    Succinyl-CoA:3-ketoacid coenzyme A transferase (SCOT): development of an antibody to human SCOT and diagnostic use in hereditary SCOT deficiency (1997), Biochim. Biophys. Acta, 1360, 151-156.
    View publication on PubMed

Cloned(Commentary)

Cloned (Comment) Organism
-
Homo sapiens

General Stability

General Stability Organism
enzyme is only soluble under denaturating conditions Homo sapiens

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
52000
-
SDS-PAGE Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
succinyl-CoA + acetoacetate Homo sapiens enzyme deficiency leads to ketoacidotic crises and persistent ketosis ?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
SCOT-deficient patients
-
Homo sapiens
-
healthy and SCOT-deficient patients
-

Source Tissue

Source Tissue Comment Organism Textmining
fibroblast
-
Homo sapiens
-
lymphocyte
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
succinyl-CoA + acetoacetate
-
Homo sapiens succinate + acetoacetyl-CoA
-
?
succinyl-CoA + acetoacetate enzyme deficiency leads to ketoacidotic crises and persistent ketosis Homo sapiens ?
-
?