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Literature summary for 2.8.3.5 extracted from

  • Kassovska-Bratinova, S.; Fukao, T.; Song, X.Q.; Duncan, A.M.V.; Chen, H.S.; Robert, M.F.; Perez-Cerda, C.; Ugarte, M.; Chartrand, C.; et al.
    Succinyl CoA:3-oxoacid CoA transferase (SCOT): human cDNA cloning, human chromosomal mapping to 5p13, and mutation detection in a SCOT-deficient patient (1996), Am. J. Hum. Genet., 59, 519-528.
    View publication on PubMedView publication on EuropePMC

Localization

Localization Comment Organism GeneOntology No. Textmining

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
succinyl-CoA + acetoacetate Homo sapiens rate determining step of ketolysis in extrahepatic tissues ?
-
?
succinyl-CoA + acetoacetate Homo sapiens enzyme deficiency leads to ketoacidotic crises and persistent ketosis ?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
SCOT-deficient patients
-

Source Tissue

Source Tissue Comment Organism Textmining
fibroblast
-
Homo sapiens
-
heart
-
Homo sapiens
-
leukocyte
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
succinyl-CoA + acetoacetate rate determining step of ketolysis in extrahepatic tissues Homo sapiens ?
-
?
succinyl-CoA + acetoacetate enzyme deficiency leads to ketoacidotic crises and persistent ketosis Homo sapiens ?
-
?