Application | Comment | Organism |
---|---|---|
medicine | GAMT is a key enzyme in the biosynthesis of creatine, deficiency leads to severe clinical symptoms, including mental retardation, muscle hypotonia, extrapyramidal movement abnormalities and epileptic seizures | Mus musculus |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
S-adenosyl-L-methionine + guanidinoacetate | Mus musculus | - |
S-adenosyl-L-homocysteine + creatine | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Mus musculus | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
brain | - |
Mus musculus | - |
cerebellum | - |
Mus musculus | - |
hippocampus | - |
Mus musculus | - |
skeletal muscle | hind leg muscle | Mus musculus | - |
thalamus | - |
Mus musculus | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
S-adenosyl-L-methionine + guanidinoacetate | - |
Mus musculus | S-adenosyl-L-homocysteine + creatine | - |
? |
Synonyms | Comment | Organism |
---|---|---|
GAMT | - |
Mus musculus |
guanidinoacetate methyltransferase | - |
Mus musculus |
guanidinoacetate N-methyltransferase | - |
Mus musculus |