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Literature summary for 6.4.1.3 extracted from

  • Kelson, T.L.; Ohura, T.; Kraus, J.P.
    Chaperonin-mediated assembly of wild-type and mutant subunits of human propionyl-CoA carboxylase expressed in Escherichia coli (1996), Hum. Mol. Genet., 5, 331-337.
    View publication on PubMed

Cloned(Commentary)

Cloned (Comment) Organism
expression of alpha and beta subunit in Escherichia coli Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
additional information Homo sapiens inherited deficiency of the enzyme activity leads to propionicacidemia ?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
ATP + propanoyl-CoA + HCO3-
-
Homo sapiens ADP + phosphate + methylmalonyl-CoA
-
?
additional information inherited deficiency of the enzyme activity leads to propionicacidemia Homo sapiens ?
-
?