Any feedback?
Please rate this page
(literature.php)
(0/150)

BRENDA support

Literature summary for 5.1.3.2 extracted from

  • Prodan-Zitnik, I.; Karas-Kuzelicki, N.; Lukac-Bajalo, J.
    Positive correlation between galactose-1-phosphate uridyltransferase (GALT) and UDP-galactose-4-epimerase (GALE) activities (2009), Clin. Biochem., 42, 1561-1564.
    View publication on PubMed

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
UDP-alpha-D-glucose Homo sapiens
-
UDP-alpha-D-galactose
-
r

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
erythrocyte
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
UDP-alpha-D-glucose
-
Homo sapiens UDP-alpha-D-galactose
-
r

Synonyms

Synonyms Comment Organism
GalE
-
Homo sapiens
UDP-galactose-4'-epimerase
-
Homo sapiens
UDP-galactose-4-epimerase
-
Homo sapiens

Temperature Optimum [°C]

Temperature Optimum [°C] Temperature Optimum Maximum [°C] Comment Organism
37
-
assay at Homo sapiens

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
9.5
-
assay at Homo sapiens

General Information

General Information Comment Organism
malfunction GALE deficiency leads to mild or severe disease with clinical symptoms similar to classical galactosemia Homo sapiens
metabolism GALE catalyzes the third step of the Leloir pathway of galactose metabolism Homo sapiens