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Literature summary for 3.2.1.52 extracted from

  • Arfi, A.; Zisling, R.; Richard, E.; Batista, L.; Poenaru, L.; Futerman, A.H.; Caillaud, C.
    Reversion of the biochemical defects in murine embryonic Sandhoff neurons using a bicistronic lentiviral vector encoding hexosaminidase alpha and beta (2006), J. Neurochem., 96, 1572-1579.
    View publication on PubMed

Application

Application Comment Organism
medicine therapeutic approach for Sandhoff disease Mus musculus

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
neuronal cell line
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
p-nitrophenyl-N-acetyl-D-glucosamine + H2O
-
Mus musculus N-acetyl-D-glucosamine + p-nitrophenol
-
?

Synonyms

Synonyms Comment Organism
beta-hexosaminidase
-
Mus musculus
hexosaminidase A
-
Mus musculus
hexosaminidase B
-
Mus musculus

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
4.5
-
-
Mus musculus