Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|
lysosome | - |
Homo sapiens | 5764 | - |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
N-acetyl-beta-D-hexosaminides + H2O | Homo sapiens | - |
N-acetyl-D-hexosamines | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
patients with I-cell disease and healthy persons | - |
Posttranslational Modification | Comment | Organism |
---|---|---|
glycoprotein | carbohydrate modification | Homo sapiens |
glycoprotein | carbohydrate units on enzymes isolated from I-cell or Pseudo-Hurler patients show modification to hybrid- or complex-type oligosaccharide | Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
lymphoblast | - |
Homo sapiens | - |
Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|
0.0024 | 0.01 | light lysosomal fraction, I-cell | Homo sapiens |
0.0032 | 0.008 | light lysosomal fraction, normal | Homo sapiens |
0.0033 | 0.0066 | light lysosomal fraction, Pseudo-Hurler | Homo sapiens |
0.0051 | 0.0079 | heavy lysosomal fraction, I-cell | Homo sapiens |
0.0061 | 0.0075 | heavy lysosomal fraction, Pseudo-Hurler | Homo sapiens |
0.0061 | 0.0211 | heavy lysosomal fraction, normal | Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
4-methylumbelliferyl-2-acetamido-2-deoxy-beta-D-galactopyranoside + H2O | - |
Homo sapiens | 4-methylumbelliferone + 2-acetamido-2-deoxy-beta-D-galactopyranoside | - |
? | |
4-methylumbelliferyl-2-acetamido-2-deoxy-beta-D-glucopyranoside + H2O | - |
Homo sapiens | 4-methylumbelliferone + 2-acetamido-2-deoxy-beta-D-glucopyranoside | - |
? | |
N-acetyl-beta-D-hexosaminides + H2O | - |
Homo sapiens | N-acetyl-D-hexosamines | - |
? |