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Literature summary for 3.1.6.13 extracted from

  • Bach, G.; Eisenberg, F., Jr.; Cantz, M.; Neufeld, E.F.
    The defect in the Hunter syndrome: deficiency of sulfoiduronate sulfatase (1973), Proc. Natl. Acad. Sci. USA, 70, 2134-2138.
    View publication on PubMedView publication on EuropePMC

Application

Application Comment Organism
medicine deficiency in Hunters syndrome, mucopolysaccharidosis II Homo sapiens

Localization

Localization Comment Organism GeneOntology No. Textmining
lysosome
-
Homo sapiens 5764
-

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
dermatan sulfate + H2O Homo sapiens
-
dermatan + sulfate
-
?
heparan sulfate + H2O Homo sapiens
-
dermatan + sulfate
-
?
heparin + H2O Homo sapiens
-
desulfated heparin + sulfate
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
skin cultured fibroblasts Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
dermatan sulfate + H2O
-
Homo sapiens dermatan + sulfate
-
?
heparan sulfate + H2O
-
Homo sapiens dermatan + sulfate
-
?
heparin + H2O
-
Homo sapiens desulfated heparin + sulfate
-
?
O-(alpha-L-idopyranosyluronic acid 2-sulfate)-(1-4)-2,5-anhydro-D-mannitol 6-sulfate + H2O
-
Homo sapiens O-(alpha-L-idopyranosyluronic acid)-(1-4)-2,5-anhydro-D-mannitol 6-sulfate + sulfate
-
?

Synonyms

Synonyms Comment Organism
Hunter corrective factor in combination with L-iduronidase Homo sapiens